Acrodermatitis enteropathica (Brandt syndrome, Danbolt – Close syndrome, Danbolt syndrome, Danbolt’s syndrome, Hereditary acrodermatitis enterohepatica, Primary zinc malabsorption)
Actinic prurigo (solar dermatitis, solar prurigo, hereditary polymorphic light eruption, familial actinic prurigo)
Aphthous Stomatitis (Canker Sores, Recurrent Aphthous Stomatitis, Simple Aphthosis, Complex Aphthosis)
Becker's nevus (Becker's melanosis, Becker's pigmentary hamartoma, nevoid melanosis, pigmented hairy epidermal nevus)
Bowenoid Papulosis (Penile Intraepithelial Neoplasia, Squamous Intraepithelial Lesion, Squamous Cell Carcinoma In Situ)
Bullous congenital ichthyosiform erythroderma (epidermolytic hyperkeratosis, keratinopathic ichthyosis)
Buschke-Ollendorff syndrome (dermatofibrosis lenticularis disseminata, connective tissue nevus with osteopoikilosis)
Central Centrifugal Cicatricial Alopecia (Hot comb alopecia, Follicular degeneration syndrome, Scarring alopecia of African-American women, Hot oil alopecia, Cosmetic alopecia, Central elliptical pseudopelade)
Chondrodermatitis Nodularis Helicis (Chondrodermatitis, Chondrodermatitis nodularis chronica helicis, Chondrodermatitis nodularis chronica helicis et antihelicis, Ear corn)
Chronic Mucocutaneous Candidiasis (candidiasis of unspecified site), unspecified disorder of immune mechanism)
Chronic actinic dermatitis (persistent light reaction, actinic reticuloid, photosensitivity dermatitis, photosensitive eczema, photosensitivity and actinic reticuloid (PD/AR) syndrome)
Clear cell acanthoma (Pale cell acanthoma, Degos acanthoma, and Acanthome cellules claires of Degos and Civatte)
Congenital Ichthyosiform Erythroderma (Nonbullous Congenital Ichthyosiform Erythroderma, Autosomal Recessive Congenital Ichthyosis)
Conradi-Hünermann syndrome (CDPX2, chondrodysplasia punctata 2; chondrodysplasia punctata, X-linked dominant form; Conradi-Hünermann-Happle syndrome, Happle syndrome)
Contact Urticaria Syndrome (Contact Urticaria, Nonimmunologic Contact Urticaria, Immunologic Contact Urticaria, Protein Contact Dermatitis)
Corn/callus (singular: callus, callosity, tyloma; plural: callosities, tylomas, tylomata) Clavus (clavi; singular: clavus, corn, heloma; plural: corns, helomas, helomata)
Cowden Syndrome (PTEN Hamartoma Tumor Syndrome, Multiple Hamartoma Syndrome, Bannayan-Riley-Ruvalcaba Syndrome, Lhermitte-Duclos Syndrome)
Cryofibrinogenemia (cold-related gelling or agglutination, Cutaneous manifestations of microvascular occlusion syndromes
Cryoglobulinemia (Cold-related gelling, Cold- related agglutination, Cutaneous manifestations of microvascular occlusion syndromes, Cryoglobulinemic syndrome [clinically asymptomatic]), Cryoglobulinemic vasculitis (clinically apparent disease process)
Cryopyrin Associated Periodic Syndrome (Familial Cold Urticaria, Familial Cold Autoinflammatory Syndrome, Muckle Wells Syndrome, Neonatal Onset Multisystem Inflammatory Disorder, Chronic Infantile Neurologic Cutaneous and Articular Syndrome)
Cutaneous Endometriosis (umbilical endometriosis,cicatricial endometriosis, endometrioma, or ectopic endometrial tissue)
Cutaneous Reactive Angiomatoses (Angioendotheliomatosis, Diffuse Dermal Angiomatosis, Acroangiodermatitis)
Cutaneous lupus mucinosis (Papulonodular mucinosis, papular and nodular mucinosis of lupus, papular and nodular mucinosis of Gold)
Cutaneous lymphoid hyperplasia (lymphocytoma cutis, lymphadenosis benigna cutis, cutaneous lymphoplasia, pseudolymphoma of Spiegler-Fendt)
Dabska tumor (Dabska-type Hemangioendothelioma Endovascular Papillary Angioendothelioma, Hobnail Hemangioendothelioma, Malignant Endovascular Papillary Angioendothelioma, Papillary Intralymphatic Angioendothelioma)
Degos Disease (Kohlmeier Disease, Degos-Kohlmeier Disease, Malignant atrophic papulosis, benign atrophic papulosis, Malignant atrophic papulosis)
Demodicidosis (Other acariasis, including chiggers and Demodex folliculorum or Trombicula infestation)
Dissecting cellulitis of the scalp (perifolliculitis abscedens et suffodiens, Hoffman disease, dissecting folliculitis, follicular occlusion triad)
Dystrophia Unguium Mediana Canaliformis (Canaliform dystrophy of the nails, Canal-like median dystrophy, Dystrophia mediana canaliformis, Dystrophia unguium mediana canaliformis of Heller, Lateral canal-like dystrophy, longitudinal single nail groove, Median canaliform dystrophy, median canaliform nail dystrophy, median canal-like dystrophy of the nail, median nail dystrophy, naevus striatus symmetricus of the thumbs.
Ecthyma gangrenosum (dermatitis gangrenosa infantum, disseminated cutaneous gangrene, pemphigus gangrenosus, rupia escharotica; Septicemia due to Pseudomonas)
Encephalocele (Cephalocele; Encephalocystocele; Encephalomyelocele; Hydroencephalocele; Hydromeningocele, cranial; Meningocele; Meningoencephalocele)
Epidermal Nevus, including Inflammatory Linear Verrucous Epidermal Nevus (Nevus Verrucosus, Dermatitic Epidermal Nevus)
Erosive Pustular Dermatitis Of The Scalp (Erosive pustulosis of the scalp, Erosive pustular dermatosis of the scalp, Pustular dermatitis of the scalp)
Erythrokeratodermia variabilis (erythrokeratodermia figurate Variabilis, erythrokeratoderma congenitals progressiva symmetrica, erythrokeratoderma progressive)
Erythropoietic Protoporphyria (Protoporphyria, Heme synthetase deficiency, Ferrochelatase deficiency, X-linked dominant protoporphyria [XLDPP], Erythrohepatic protoporphyria [no longer used])
Eyelid Dermatitis (xeroderma of the eyelids, eczema of the eyelids, atopic dermatitis, allergic contact dermatitis, irritant contact dermatitis, seborrheic dermatitis of the eyelids)
Fabry Disease (Anderson-Fabry Disease, Alpha-Galactosidase A Deficiency, Angiokeratoma Corporis Diffusum, Ceramide Trihexosidase Deficiency, Fabry's Disease, GLA Deficiency, Hereditary Dystopic Lipidosis)
Familial Cutaneous Leiomyomatosis (FCL) (Hereditary Multiple Leiomyomas, Hereditary Leiomyomatosis and Renal Cell Cancer [HLRCC], Multiple Cutaneous and Uterine Leiomyomatosis, Reed Syndrome)
Favre-Racouchot Syndrome (Nodular Elastosis [Elastoidosis] with Cysts and Comedones, Senile or Solar Comedones, Smokers' Comedones)
Green Nail Syndrome (GNS, Pseudomonas nail infection, chloronychia, green striped nails, chromonychia)
Melanocytic Nevi, Including Atypical Nevi (Dysplastic Nevi, Nevus with Architectural disorder and Cytologic Atypia)
Mucous Cysts (mucoid cyst, mucinous pseudocyst, myxomatous cutaneous cyst, synovial cyst, periungual ganglion, nail cyst, digital myxoid cyst, cutaneous myxoid cyst
Necrotic Drug eruptions (Heparin-induced skin necrosis; warfarin-induced skin necrosis (Coumadin® necrosis)
Rubinstein – Taybi Syndrome (Rubinstein syndrome, broad thumb-hallux syndrome, broad thumbs and great toes, characteristic facies and mental retardation)
Systemic Amyloidosis with Cutaneous Manifestations (Amyloidosis, Primary Systemic Amyloidosis, AL Amyloidosis)
Systemic Contact Dermatitis (Contact Dermatitis, Systemic; Baboon syndrome; Fisher's systemic contact dermatitis; Systemic contact-type dermatitis; Hematogenous contact eczema; Symmetrical Drug-Related Intertriginous and Flexural Exanthem [SDRIFE] Systemic reactivation of allergic contact dermatitis [RCD])
Wiskott-Aldrich Syndrome (Wiskott-Aldrich-Huntley syndrome, eczema-thrombocytopenia-immunodeficiency syndrome)
Xanthoma, eruptive (hyperchylomicronemia, Fredrickson type I hyperlipoproteinemia, Fredrickson type V hyperlipoproteinemia)
Xanthomas, plane (planar xanthoma, palmar xanthoma, intertriginous xanthoma, diffuse xanthoma, xanthelasma)