Congenital Ichthyosiform Erythroderma (Nonbullous Congenital Ichthyosiform Erythroderma, Autosomal Recessive Congenital Ichthyosis)
Are You Confident of the Diagnosis? What you should be alert for in the history Congenital ichthyosiform erythroderma (CIE) may present in the newborn period as a collodion baby (milder than with lamellar ichthyosis) with ectropion and eclabium (Figure 1). As the collodion membrane is shed, patients develop diffuse erythema and fine, powdery scaling and…